Degenerative disorder of the cochlear resulting in hearing loss

Aetiology

• Typically seen in old age, although onset can be variable
• Can be due to:
  • Loss of outer hair cells - environmental noise toxicity over time is a major factor
  • Loss of ganglion cells
  • Strial atrophy

Clinical features

• Gradual onset hearing loss

Investigations

• Audiometry:
  • Higher frequencies affected most
  • Usually sensorineural hearing loss

Management

• High-frequency-specific hearing aid